Pathophysiology[ edit ] Being idiopathic, IPH by definition has an unknown cause. It is thought to be an immune-mediated disease. Meanwhile, there is insufficient iron for inclusion into the haemoglobin molecules inside red blood cells which carry oxygen to body tissues for cellular respiration. Idiopathic pulmonary haemosiderosis can occur either as a primary lung disorder or as the sequela to other pulmonary, cardiovascular or immune system disorder. PH3 involves no demonstrable immune system involvement. This is called Heiner syndrome.
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These resources provide more information about this condition or associated symptoms. The in-depth resources contain medical and scientific language that may be hard to understand. You may want to review these resources with a medical professional. In-Depth Information Medscape Reference provides information on this topic. You may need to register to view the medical textbook, but registration is free. The Monarch Initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers.
This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health. Visit the website to explore the biology of this condition. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers.
Access to this database is free of charge. PubMed is a searchable database of medical literature and lists journal articles that discuss Idiopathic pulmonary hemosiderosis. Click on the link to view a sample search on this topic. We remove all identifying information when posting a question to protect your privacy. If you do not want your question posted, please let us know. A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis. Orphanet J Rare Dis. August 20, ; New insights into pediatric idiopathic pulmonary hemosiderosis: the French RepsiRare cohort.
Orphanet Journal of Rare Diseases. Schwarz MI. Idiopathic Pulmonary Hemosiderosis. Merck Manual. Pulmonary Hemosiderosis. Online Mendelian Inheritance in Man. Idiopathic pulmonary hemosiderosis. Idiopathic pulmonary hemosiderosis in adults: review of cases reported in the latest 15 years. The Clinical Respiratory Journal. Idiopathic pulmonary hemosiderosis in adult. Respiratory Medicine CME.
Idiopathic pulmonary haemosiderosis
References Epidemiology It is rare disorder that can occur at any age but typically affects children and young adults. The age of presentation may be bimodal, with frequency peaks in children less than five years of age and in adolescents 11 years or older. There is no definite recognized gender predilection. Pathology Hemosiderin-laden macrophages are found in the sputum or at bronchoalveolar lavage.
Hemosiderosis Pulmonar Idiopática
Idiopathic pulmonary hemosiderosis